Ubiquitin carboxyl-terminal hydrolase 19 (USP19)

Deubiquitinating enzyme that regulates the degradation of various proteins. Deubiquitinates and prevents proteasomal degradation of RNF123 which in turn arouses CDKN1B ubiquitin- dependent degradation thereby playing a role in cell proliferation.

Modulates transcription of major myofibrillar proteins. Also involved in turnover of endoplasmic- reticulum-associated degradation (ERAD) substrates.