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- Table of Contents
Designing a Western blot for CPS1? The guide has the expected band size, antibodies backed by real blot images, the controls to run alongside, and protocols taken from published papers.
Open the CPS1 Western Blot GuideDesigning an IHC experiment for CPS1? The guide has the expected staining pattern, antigen retrieval and fixation, antibodies backed by real IHC images, the tissue controls to run alongside, and protocols taken from published papers.
Open the CPS1 IHC GuideFacts about Carbamoyl-phosphate synthase [ammonia], mitochondrial.
| Human | |
|---|---|
| Gene Name: | CPS1 |
| Uniprot: | P31327 |
| Entrez: | 1373 |

| Belongs to: |
|---|
| No superfamily |

carbamoyl-phosphate synthase [ammonia], mitochondrial; carbamoyl-phosphate synthase 1, mitochondrial; carbamoyl-phosphate synthetase 1, mitochondrial; carbamoylphosphate synthetase I; Carbamoyl-phosphate synthetase I; CPSase I; CPSASE1; EC 6.3.4.16
Mass (kDA):
164.939 kDA

| Human | |
|---|---|
| Location: | 2q34 |
| Sequence: | 2; NC_000002.12 (210477685..210679107) |
Primarily in the liver and small intestine.
Mitochondrion. Nucleus, nucleolus.





PMID: 1840546 by Haraguchi Y., et al. Cloning and sequence of a cDNA encoding human carbamyl phosphate synthetase I: molecular analysis of hyperammonemia.
PMID: 9711878 by Finckh U., et al. Prenatal diagnosis of carbamoyl phosphate synthetase I deficiency by identification of a missense mutation in CPS1.
*More publications can be found for each product on its corresponding product page